| Defective B3GAT3 causes JDSSDHD | R-HSA-3560801 | 8.66 |
| CS/DS degradation | R-HSA-2024101 | 9.18 |
| Metabolism of carbohydrates | R-HSA-71387 | 4.93 |
| Dermatan sulfate biosynthesis | R-HSA-2022923 | 9.52 |
| Chondroitin sulfate/dermatan sulfate metabolism | R-HSA-1793185 | 7.34 |
| Defective CHST14 causes EDS, musculocontractural type | R-HSA-3595174 | 9.98 |
| Defective CHSY1 causes TPBS | R-HSA-3595177 | 9.98 |
| Diseases associated with glycosaminoglycan metabolism | R-HSA-3560782 | 7.77 |
| Defective B4GALT7 causes EDS, progeroid type | R-HSA-3560783 | 8.66 |
| Defective CHST3 causes SEDCJD | R-HSA-3595172 | 9.98 |
| ECM proteoglycans | R-HSA-3000178 | 6.75 |
| Extracellular matrix organization | R-HSA-1474244 | 4.91 |
| Metabolism | R-HSA-1430728 | 2.34 |
| A tetrasaccharide linker sequence is required for GAG synthesis | R-HSA-1971475 | 8.28 |
| Glycosaminoglycan metabolism | R-HSA-1630316 | 6.04 |
| Heparan sulfate/heparin (HS-GAG) metabolism | R-HSA-1638091 | 7.2 |
| Diseases of glycosylation | R-HSA-3781865 | 6.89 |
| Chondroitin sulfate biosynthesis | R-HSA-2022870 | 8.66 |
| Disease | R-HSA-1643685 | 3.33 |