Gene | Associated with CARNEY TRIAD in | Link to HGNC | Cytogenetic band | Number of associated diseases | Associated diseases |
---|---|---|---|---|---|
SDHA | ClinVar | HGNC link | 5p15.33 | 5 | 252011, 604287, PS115200, PS168000, 256000 |
SDHC | ClinVar | HGNC link | 1q23.3 | 4 | 604287, 606864, PS168000, 606764 |
SDHB | ClinVar | HGNC link | 1p36.13 | 6 | 171300, 604287, 606764, 606864, PS168000, PS158350 |
Download the disease annotation in CSV format
regulated gene | associated to this disease | # TFs | TFs | # TFs associated with this disease | TFs associated with this disease |
---|---|---|---|---|---|
SDHB | YES | 4 | NRF1, NFE2L2, PLAGL1, HIF1A | 0 |
Gene1 | Gene2 | Direct Interaction | Number of shared interactors | Shared genes in interaction |
---|---|---|---|---|
SDHA | SDHC | Yes | 3 | NDUFS2, XRCC6, SDHB |
SDHA | SDHB | Yes | 24 | NDUFS8, NDUFV2, CUL1, SDHC, UQCRB, CS, UBXN10, MDH2, TIMM50, COPS5, NDUFV1, ITGA4, DLD, OTUB1, PDHA1, SUCLG1, CUL2, ACLY, SUCLA2, CAND1, ACAT1, NDUFA2, UQCRFS1, CUL3 |
SDHC | SDHB | Yes | 2 | MTCH2, SDHA |
Direct interactions graph
Interactions graph (direct and indirect interactions, when direct are not available)
Gene1 | Gene2 | Direct Interaction | Interaction mode | Number of shared interactors | Shared genes in interaction |
---|---|---|---|---|---|
SDHA | SDHC | Yes | binding | 3 | UBC, SDHD, SDHB |
SDHA | SDHB | Yes | binding | 3 | UBC, SDHC, SDHD |
SDHC | SDHB | Yes | binding | 3 | UBC, SDHD, SDHA |
Direct interactions graph
Interactions graph (direct and indirect interactions, when direct are not available)
Gene1 | Gene2 | Direct Interaction | Number of shared interactors | Shared genes in interaction |
---|---|---|---|---|
SDHA | SDHB | Yes | 4 | ACAT1, TIMM50, UQCRFS1, NDUFV2 |
Direct interactions graph
Interactions graph (direct and indirect interactions, when direct are not available)
Gene1 | Gene2 | Direct interaction | More information |
---|---|---|---|
SDHA | SDHB | yes, complex | Components of complex composed of four subunits: the flavoprotein (FP) SDHA, iron-sulfur protein (IP) SDHB, and a cytochrome b560 composed of SDHC and SDHD. [UniProt] |
SDHA | SDHC | yes, complex | Components of complex composed of four subunits: the flavoprotein (FP) SDHA, iron-sulfur protein (IP) SDHB, and a cytochrome b560 composed of SDHC and SDHD. [UniProt] |
SDHB | SDHC | yes, complex | Components of complex composed of four subunits: the flavoprotein (FP) SDHA, iron-sulfur protein (IP) SDHB, and a cytochrome b560 composed of SDHC and SDHD. [UniProt] |
KEGG term | KEGG term ID | IC | Number of genes with the same term | Genes |
---|---|---|---|---|
Oxidative phosphorylation | hsa00190 | 5.69 | 3 | SDHC, SDHB, SDHA |
Metabolic pathways | hsa01100 | 2.49 | 3 | SDHC, SDHB, SDHA |
Carbon metabolism | hsa01200 | 6.03 | 3 | SDHC, SDHB, SDHA |
Citrate cycle (TCA cycle) | hsa00020 | 7.86 | 3 | SDHC, SDHB, SDHA |
Non-alcoholic fatty liver disease (NAFLD) | hsa04932 | 5.51 | 3 | SDHC, SDHB, SDHA |
Huntington's disease | hsa05016 | 5.17 | 3 | SDHC, SDHB, SDHA |
Alzheimer's disease | hsa05010 | 5.34 | 3 | SDHC, SDHB, SDHA |
Parkinson's disease | hsa05012 | 5.59 | 3 | SDHC, SDHB, SDHA |
Term | New enriched term | IC | P value | Genes |
---|---|---|---|---|
Neurodegenerative diseases | NEW | 4.27 | 0.002 | SDHC, SDHB, SDHA |
Endocrine and metabolic diseases | NEW | 4.75 | 0.005 | SDHC, SDHB, SDHA |
Oxidative phosphorylation (hsa00190) | - | 5.69 | 0.0 | SDHC, SDHB, SDHA |
Parkinson's disease (hsa05012) | - | 5.59 | 0.0 | SDHC, SDHB, SDHA |
Energy metabolism | NEW | 5.42 | 0.0 | SDHC, SDHB, SDHA |
Carbohydrate metabolism | NEW | 4.36 | 0.002 | SDHC, SDHB, SDHA |
Carbon metabolism (hsa01200) | - | 6.03 | 0.0 | SDHC, SDHB, SDHA |
Non-alcoholic fatty liver disease (NAFLD) (hsa04932) | - | 5.51 | 0.0 | SDHC, SDHB, SDHA |
Huntington's disease (hsa05016) | - | 5.17 | 0.001 | SDHC, SDHB, SDHA |
Alzheimer's disease (hsa05010) | - | 5.34 | 0.0 | SDHC, SDHB, SDHA |
Citrate cycle (TCA cycle) (hsa00020) | - | 7.86 | 0.0 | SDHC, SDHB, SDHA |
REACTOME term | REACTOME term ID | IC | Number of genes with the same term | Genes |
---|---|---|---|---|
Respiratory electron transport | R-HSA-611105 | 6.44 | 3 | SDHC, SDHB, SDHA |
Pyruvate metabolism and Citric Acid (TCA) cycle | R-HSA-71406 | 7.56 | 3 | SDHC, SDHB, SDHA |
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. | R-HSA-163200 | 6.12 | 3 | SDHC, SDHB, SDHA |
Citric acid cycle (TCA cycle) | R-HSA-71403 | 8.73 | 3 | SDHC, SDHB, SDHA |
The citric acid (TCA) cycle and respiratory electron transport | R-HSA-1428517 | 5.71 | 3 | SDHC, SDHB, SDHA |
Metabolism | R-HSA-1430728 | 2.34 | 3 | SDHC, SDHB, SDHA |
Term | New enriched term | IC | P value | Genes |
---|---|---|---|---|
succinate dehydrogenase activity (GO:0000104) | - | 8.13 | 0.0 | SDHC, SDHB, SDHA |
tetrapyrrole binding (GO:0046906) | NEW | 4.8 | 0.024 | SDHC, SDHA |
oxidoreductase activity, acting on the CH-CH group of donors (GO:0016627) | - | 5.66 | 0.0 | SDHC, SDHB, SDHA |
oxidoreductase activity, acting on the CH-CH group of donors, quinone or related compound as acceptor (GO:0016635) | - | 8.64 | 0.0 | SDHB, SDHA |
cofactor binding (GO:0048037) | - | 4.16 | 0.025 | SDHB, SDHA |
succinate dehydrogenase (ubiquinone) activity (GO:0008177) | - | 9.05 | 0.0 | SDHB, SDHA |
oxidoreductase activity (GO:0016491) | - | 3.12 | 0.029 | SDHC, SDHB, SDHA |
electron carrier activity (GO:0009055) | - | 4.97 | 0.003 | SDHC, SDHB |
Term | New enriched term | IC | P value | Genes |
---|---|---|---|---|
dicarboxylic acid metabolic process (GO:0043648) | - | 5.3 | 0.005 | SDHB, SDHA |
aerobic respiration (GO:0009060) | - | 6.4 | 0.0 | SDHC, SDHB |
energy derivation by oxidation of organic compounds (GO:0015980) | - | 4.93 | 0.043 | SDHC, SDHB |
succinate metabolic process (GO:0006105) | - | 7.43 | 0.0 | SDHB, SDHA |
tricarboxylic acid cycle (GO:0006099) | - | 6.33 | 0.0 | SDHC, SDHB, SDHA |
electron transport chain (GO:0022900) | - | 5.09 | 0.0 | SDHC, SDHB, SDHA |
cellular respiration (GO:0045333) | - | 5.9 | 0.001 | SDHC, SDHB |
respiratory electron transport chain (GO:0022904) | - | 5.11 | 0.0 | SDHC, SDHB, SDHA |
generation of precursor metabolites and energy (GO:0006091) | - | 4.07 | 0.0 | SDHC, SDHB, SDHA |
oxidation-reduction process (GO:0055114) | - | 2.91 | 0.005 | SDHC, SDHB, SDHA |
Term | New enriched term | IC | P value | Genes |
---|---|---|---|---|
succinate dehydrogenase complex (ubiquinone) (GO:0045257) | - | 8.42 | 0.0 | SDHC, SDHB, SDHA |
catalytic complex (GO:1902494) | - | 2.9 | 0.028 | SDHC, SDHB, SDHA |
fumarate reductase complex (GO:0045283) | - | 8.42 | 0.0 | SDHC, SDHB, SDHA |
organelle inner membrane (GO:0019866) | - | 3.56 | 0.002 | SDHC, SDHB, SDHA |
succinate dehydrogenase complex (GO:0045281) | - | 8.42 | 0.0 | SDHC, SDHB, SDHA |
oxidoreductase complex (GO:1990204) | - | 5.19 | 0.0 | SDHC, SDHB, SDHA |
mitochondrial membrane part (GO:0044455) | - | 4.54 | 0.0 | SDHC, SDHB, SDHA |
mitochondrial inner membrane (GO:0005743) | - | 3.65 | 0.001 | SDHC, SDHB, SDHA |
mitochondrion (GO:0005739) | - | 2.42 | 0.01 | SDHC, SDHB, SDHA |
mitochondrial respiratory chain complex II (GO:0005749) | - | 8.42 | 0.0 | SDHC, SDHB, SDHA |
mitochondrial membrane (GO:0031966) | - | 3.31 | 0.001 | SDHC, SDHB, SDHA |
mitochondrial part (GO:0044429) | - | 2.92 | 0.025 | SDHC, SDHB, SDHA |