Disease table of MITOCHONDRIAL COMPLEX I DEFICIENCY OMIM ID: 252010

Gene-disease associations table

GeneAssociated with MITOCHONDRIAL COMPLEX I DEFICIENCY inLink to HGNCCytogenetic bandNumber of associated diseasesAssociated diseases
NDUFB9OMIMHGNC link8q24.131252010
NDUFB3OMIMHGNC link2q33.11252010
NUBPLOMIM, HUMSAVARHGNC link14q121252010
NDUFAF5OMIM, HUMSAVARHGNC link20p12.12256000, 252010
NDUFAF4OMIM, HUMSAVARHGNC link6q16.11252010
NDUFAF6HUMSAVARHGNC link8q22.12256000, 252010
NDUFAF1OMIMHGNC link15q15.11252010
NDUFAF3OMIM, HUMSAVARHGNC link3p21.311252010
NDUFAF2OMIMHGNC link5q12.12256000, 252010
NDUFV2OMIMHGNC link18p11.221252010
NDUFV1OMIM, HUMSAVARHGNC link11q13.22256000, 252010
MT-ND3HUMSAVARHGNC linkMT3256000, 252010, 500001
MT-ND5HUMSAVARHGNC linkMT6535000, 256000, 520100, 540000, 545000, 252010
MT-ND6HUMSAVARHGNC linkMT5535000, 553000, 540000, 252010, 500001
NDUFA1OMIM, HUMSAVARHGNC linkXq241252010
FOXRED1OMIM, HUMSAVARHGNC link11q24.22256000, 252010
NDUFA11OMIMHGNC link19p13.31252010
MT-ND1HUMSAVARHGNC linkMT6500008, 535000, 540000, 500001, 502500, 252010
NDUFS1OMIM, HUMSAVARHGNC link2q33.32540000, 252010
NDUFS2OMIM, HUMSAVARHGNC link1q23.31252010
NDUFS3OMIMHGNC link11p11.22256000, 252010
NDUFS4OMIMHGNC link5q11.22256000, 252010
NDUFS6OMIMHGNC link5p15.331252010
NDUFS7HUMSAVARHGNC link19p13.32256000, 252010

Download the disease annotation in CSV format

Relations among genes:

Tandem repeat annotations from DGD
Cytogenetic band analysis
By sub-band
Shared sub_bandNumber of genes associated with the diseaseGenes associated with the disease
19p13.32NDUFS7, NDUFA11
By band
Shared bandNumber of genes associated with the diseaseGenes associated with the disease
2q332NDUFB3, NDUFS1
19p132NDUFS7, NDUFA11
By region
Shared regionNumber of genes associated with the diseaseGenes associated with the disease
2q32NDUFB3, NDUFS1
5q12NDUFS4, NDUFAF2
8q22NDUFB9, NDUFAF6
19p12NDUFS7, NDUFA11
By arm
Shared armNumber of genes associated with the diseaseGenes associated with the disease
2q2NDUFB3, NDUFS1
5q2NDUFS4, NDUFAF2
19p2NDUFS7, NDUFA11
11q2FOXRED1, NDUFV1
8q2NDUFB9, NDUFAF6
By chromosome
Shared chromosomeNumber of genes associated with the diseaseGenes associated with the disease
113FOXRED1, NDUFS3, NDUFV1
192NDUFS7, NDUFA11
22NDUFB3, NDUFS1
53NDUFS6, NDUFS4, NDUFAF2
82NDUFB9, NDUFAF6
Transcription Factors (TF) annotation from TRRUST
TFassociated to this disease# regulated genesRegulated genes# regulated genes associated with this diseaseRegulated genes associated with this disease
SP1NO460ITGB3, KRT14, CDK4, UGCG, PGR, GAST, PSIP1, ITGA5, PTHLH, ITGB2, CD44, HLA-G, LTF, IGFBP4, NF1, ACVRL1, GSTP1, CYP2F1, CA9, MMRN1, HSD17B2, STK11, FGFR3, CD28, UGT1A4, FASLG, DNASE2, KRT19, SLC39A1, ALOX5, PDGFB, PTGS2, CYP7A1, TNF, TPMT, HSD11B2, FMR1, CHI3L1, PCK1, DMRT1, RARA, RASSF1, CYP3A7, BRD7, CYP17A1, LPL, CXADR, PADI3, ABCA1, NR5A1, COL11A2, IRF5, XIAP, BACE1, STAR, TBX21, BSG, APP, MDM2, COMP, ALOX12, CHRNB4, SNAP25, MTA1, CCK, DDB2, CIC, ACAN, KIT, MAT2A, SERPINB5, CDH2, ICAM1, SLC29A1, USP7, SLC5A8, HTR1A, REST, IGF2, APOC3, APAF1, ABCG2, IFNGR1, CRMP1, SLC7A5, PDGFC, HNF4A, ATP2C1, MICA, EAPP, TNFRSF10B, KRT5, MACROD1, ERVW-1, CD151, ELF4, MMP28, POLD2, DNMT1, MAOB, CBS, E2F1, KCNQ3, COL18A1, HIST2H4A, RPS3A, IL10, C4A, CYP3A5, ST6GAL1, CD99, BCL2, SLC15A1, IL6, ADAM10, KRT16, POLE2, MUC6, CBFB, ACO1, DCK, CAV1, MIF, DNMT3A, HMGA2, PDIA2, B4GALT1, GJA1, PPL, SLC13A4, AGTR1, PTGIR, CETP, SLC2A2, CYP27A1, F2R, BLMH, ADIPOQ, CENPH, OPRM1, BAG2, MPO, WRN, CDK6, PTTG1, YY1, CD2AP, TBXA2R, TGM4, PRSS50, HSD17B11, HCN2, MYCN, F3, ID4, CDKN1A, SLC5A1, SERPINE1, C1QBP, SOX3, EGR1, TF, RETN, SYP, RORA, NDUFV1, C4B, SNAPC1, TGFBR2, MME, GATA3, DPYSL2, CXCL14, SPRY2, ABCB8, COX4I1, SCTR, UGDH, HBEGF, PLAT, FOS, XPC, MUC5AC, HYAL1, BRCA1, NOS1, KCTD11, HCN4, ASPN, OXTR, COL1A1, TLR2, ALOX15B, ITGAV, IL5, SLC9A2, SIRT1, FGL2, KLF8, KCNQ2, UGT2B15, FOXM1, TEC, CHST4, TINF2, SLC19A3, KIF2C, ADAM23, PTGES, DNMT3B, GCLC, THBD, GFER, ADRBK1, TGFB1, SLC25A20, TK1, PRM1, CXCL1, APOE, PDE6A, TICAM1, KCNH2, TERF2, CENPW, NFKB1, ITGA2, PCYT1A, SIGIRR, IRS2, SP3, GIPR, SCNN1B, PTN, PTEN, NDUFV2, INSR, AGT, ME1, ATP2A2, HAS2, CYP19A1, HTT, MAT2B, PRNP, MNDA, SLC9A3, ADAM17, BAX, SLC3A2, UTRN, SPN, PAX6, SMARCA1, IL2, CREM, MMP9, ENG, CHGA, MUC4, ESR1, AHR, ATM, NFKB2, COL7A1, CD97, EPO, TFPI2, POR, DRG2, ELMO3, CAT, CYP3A4, LOXL4, BDKRB1, WAS, PNOC, LDHC, ADH6, CDC42BPG, NKX2-1, CYP1B1, TAF7, PLAUR, MMP2, MMP11, APLNR, UBC, GM2A, FGFR1, PLAA, TIMP1, TNFSF14, PTK6, KISS1, CDKN2B, COL2A1, BTK, ITGAX, HBZ, CREB1, MMP14, MICB, LEP, FOLR1, ATP2A3, SNRPN, ADA, PSEN1, SPP1, TNNI3, NOL7, VEGFA, CSNK2A1, VAMP2, NQO2, LOR, EPOR, HSD3B1, ISG20, MET, F10, CD1D, FBLN1, APLP1, CCL5, FAS, ERBB2, COPS5, MYBL1, RECQL4, CD83, SOD1, HOXB7, WIF1, SLC39A8, CES1, IL5RA, APEX1, ITGAD, TNC, KDR, CLDN3, NR4A1, MYC, RELA, RECK, PGLYRP2, LRP5, MYBL2, ADRA2B, VIM, EGFR, GDA, SOD2, FES, LDHA, CD14, AMACR, IGFBP1, SLC19A1, IMPDH2, PDE6B, LCAT, PPP2R2B, FBN1, CERS2, EPAS1, KLK3, FLNA, CCL2, HMGA1, BACE2, EDNRB, FABP6, HPR, IGFBP3, PON1, APOA1, NPY, B4GALT5, FXR2, CCND2, STARD3, IL2RB, DDB1, SQSTM1, TERT, HGF, TNFSF10, KRT18, TYMP, MUC2, MPG, ABCC3, HDAC4, TCN2, TYMS, DBF4, CASP3, SGPL1, GH2, EGF, CCND1, GPR39, IVL, AR, NT5E, LYZ, SMPD1, PHGDH, CDKN2A, MGST1, CCNA2, POLD1, NOS3, ABCB1, DHCR24, LDLR, HSD17B1, SOCS1, FBP1, LTC4S, CTSL, BIRC5, HRAS, PDHA1, TIMP2, P4HA1, TMPO, ARF6, CDKN1B, SLC31A1, SOX9, PLAU, RGN, CTSB, EZR, TIMP3, F7, SREBF1, SKP2, SCT, VDR, ADRB3, CXCL5, LMO4, CD163, MCTS1, ATF2, CTGF, SRC, P2RX4, TGFA, IL3, CYP7B1, ADRA1A, GRIN1, SRY, ODC12NDUFV1, NDUFV2
regulated geneassociated to this disease# TFsTFs # TFs associated with this diseaseTFs associated with this disease
NDUFV2YES1SP10
NDUFV1YES1SP10
Interactions from BIOGRID - physical
Gene1Gene2Direct InteractionNumber of shared interactorsShared genes in interaction
NDUFB9NDUFB3No7HSPB2, ENPP6, ATP5C1, NDUFA8, NDUFA12, NDUFA9, NDUFS3
NDUFB9NDUFAF5No1NDUFS3
NDUFB9NDUFAF4No3NDUFS3, TIMMDC1, NDUFS5
NDUFB9NDUFAF1No7NDUFS5, NDUFS1, NDUFA12, NDUFA8, MAGEA11, TIMMDC1, NDUFS3
NDUFB9NDUFAF3No6NDUFB10, NDUFS5, NDUFA8, TIMMDC1, ABCC1, NDUFS3
NDUFB9NDUFV2No10NDUFB10, NDUFS5, NDUFS1, NDUFA12, NDUFA9, NDUFA2, NDUFA8, SDHB, NDUFA6, NDUFS3
NDUFB9NDUFV1No16VDAC2, ILF3, NDUFB10, TIMMDC1, NDUFS1, NDUFA12, NDUFA9, ATP5F1, NDUFA8, HSPA1L, NDUFA2, NDUFS3, SDHB, NDUFB8, NDUFS5, POR
NDUFB9NDUFA1No1NDUFA8
NDUFB9FOXRED1No2NXF1, NDUFS5
NDUFB9NDUFA11No12NDUFS5, NDUFS1, NDUFA12, NDUFA9, NDUFA5, NDUFB8, NDUFA2, HSPB2, NDUFA8, NDUFB5, NDUFA6, NDUFS3
NDUFB9NDUFS1Yes14ATP5B, CLTC, NDUFB10, NDUFS5, ATP5F1, NDUFA12, HTT, ATP5C1, NDUFA8, MTCH2, SDHB, NDUFB5, NDUFA9, NDUFS3
NDUFB9NDUFS2No11ATP5F1, NDUFS1, NDUFA12, NDUFA9, HSPA1L, NDUFA8, MTCH2, TIMMDC1, NXF1, NDUFS5, NDUFS3
NDUFB9NDUFS3Yes13NDUFB10, NDUFS1, NXF1, NDUFS5, HTT, NDUFA12, NDUFA2, NDUFA5, MTCH2, NDUFA9, NDUFB7, NDUFB8, NDUFB5
NDUFB9NDUFS4No16VDAC2, NDUFB10, NDUFS5, NDUFS1, NDUFA12, ATP5C1, PRRT2, NDUFA8, NDUFA2, ATP5O, SDHB, NDUFB8, NDUFA9, NDUFB5, NDUFS3, ATP5F1
NDUFB9NDUFS6No10ILF3, NDUFS5, NDUFS1, NDUFA12, NDUFA9, NDUFA2, NDUFA8, MPV17, NXF1, NDUFS3
NDUFB9NDUFS7No12MPV17, NDUFB10, NDUFS5, NDUFS1, NDUFA12, NDUFA9, ATP5F1, NDUFA5, NDUFA8, TIMMDC1, NDUFB5, NDUFS3
NDUFB3NDUFAF5No1NDUFS3
NDUFB3NDUFAF4No2NDUFA13, NDUFS3
NDUFB3NDUFAF1No4NDUFA8, NDUFA13, NDUFA12, NDUFS3
NDUFB3NDUFAF3No3NDUFA8, NDUFA13, NDUFS3
NDUFB3NDUFV2No6NDUFA9, NDUFA13, NDUFA11, NDUFA8, NDUFA12, NDUFS3
NDUFB3NDUFV1No6NDUFA9, NDUFA13, NDUFA11, NDUFA8, NDUFA12, NDUFS3
NDUFB3NDUFA1No1NDUFA8
NDUFB3NDUFA11Yes5NDUFA8, NDUFA9, HSPB2, NDUFS3, NDUFA12
NDUFB3NDUFS1No7ATP5C1, NDUFA13, NDUFA11, NDUFA8, NDUFA12, NDUFA9, NDUFS3
NDUFB3NDUFS2No7NDUFA9, NDUFA13, NDUFA11, NDUFA8, APP, NDUFA12, NDUFS3
NDUFB3NDUFS3Yes4NDUFA11, NDUFA9, NDUFA13, NDUFA12
NDUFB3NDUFS4No8ATP5C1, NDUFA13, NDUFA11, NDUFA8, APP, NDUFA12, NDUFA9, NDUFS3
NDUFB3NDUFS6No5NDUFA11, NDUFA8, NDUFA9, NDUFS3, NDUFA12
NDUFB3NDUFS7No6NDUFA9, NDUFA13, NDUFA11, NDUFA8, NDUFA12, NDUFS3
NUBPLNDUFV1No1DNAJB11
NUBPLNDUFS1No1RNF2
NDUFAF5NDUFAF4No3NDUFS7, NDUFAF3, NDUFS3
NDUFAF5NDUFAF1No2NDUFAF3, NDUFS3
NDUFAF5NDUFAF3Yes2NDUFS7, NDUFS3
NDUFAF5NDUFV2No3NDUFS7, NDUFA10, NDUFS3
NDUFAF5NDUFV1No3NDUFS7, NDUFA10, NDUFS3
NDUFAF5NDUFA11No3NDUFS7, NDUFA10, NDUFS3
NDUFAF5NDUFS1No2NDUFS7, NDUFS3
NDUFAF5NDUFS2No4NDUFAF3, NDUFS7, NDUFA10, NDUFS3
NDUFAF5NDUFS3Yes2NDUFS7, NDUFAF3
NDUFAF5NDUFS4No3NDUFS7, NDUFAF3, NDUFS3
NDUFAF5NDUFS6No3DTX3, NDUFS7, NDUFS3
NDUFAF5NDUFS7Yes3NDUFS7, NDUFAF3, NDUFS3
NDUFAF4NDUFAF1No6ECSIT, TIMMDC1, NDUFS5, NDUFA13, NDUFAF3, NDUFS3
NDUFAF4NDUFAF3Yes6ECSIT, NDUFS5, NDUFA13, NDUFS7, TIMMDC1, NDUFS3
NDUFAF4NDUFV2No4NDUFA13, NDUFS7, NDUFS3, NDUFS5
NDUFAF4NDUFV1No5NDUFS7, NDUFA13, NDUFS3, TIMMDC1, NDUFS5
NDUFAF4FOXRED1No1NDUFS5
NDUFAF4NDUFA11No3NDUFS7, NDUFS5, NDUFS3
NDUFAF4NDUFS1No5NDUFA13, NDUFS7, ECSIT, NDUFS3, NDUFS5
NDUFAF4NDUFS2No7ECSIT, TIMMDC1, NDUFS5, NDUFA13, NDUFS7, NDUFAF3, NDUFS3
NDUFAF4NDUFS3Yes5NDUFA13, NDUFAF3, ECSIT, NDUFS7, NDUFS5
NDUFAF4NDUFS4No5NDUFAF3, NDUFA13, NDUFS7, NDUFS3, NDUFS5
NDUFAF4NDUFS6No3NDUFS7, NDUFS5, NDUFS3
NDUFAF4NDUFS7Yes6TIMMDC1, NDUFS5, NDUFA13, NDUFS7, NDUFAF3, NDUFS3
NDUFAF1NDUFAF3Yes8ECSIT, NDUFS5, NDUFA13, NDUFB11, ACAD9, NDUFA8, TIMMDC1, NDUFS3
NDUFAF1NDUFV2No6NDUFS5, NDUFS1, NDUFA13, NDUFA8, NDUFA12, NDUFS3
NDUFAF1NDUFV1No7TIMMDC1, NDUFS1, NDUFA13, NDUFA8, NDUFA12, NDUFS5, NDUFS3
NDUFAF1NDUFA1No1NDUFA8
NDUFAF1FOXRED1No1NDUFS5
NDUFAF1NDUFA11No6NDUFA12, NDUFS1, NDUFB11, NDUFA8, NDUFS5, NDUFS3
NDUFAF1NDUFS1Yes7ECSIT, NDUFS5, NDUFA13, TMEM126B, NDUFA8, NDUFA12, NDUFS3
NDUFAF1NDUFS2No11ECSIT, TIMMDC1, NDUFS1, NDUFAF3, NDUFA13, ACAD9, NDUFA8, NDUFA12, FAF2, NDUFS5, NDUFS3
NDUFAF1NDUFS3Yes9ECSIT, NDUFS5, NDUFS1, NDUFA12, NDUFA13, NDUFB11, ACAD9, TMEM126B, NDUFAF3
NDUFAF1NDUFS4No7NDUFAF3, NDUFS1, NDUFA13, NDUFA8, NDUFA12, NDUFS5, NDUFS3
NDUFAF1NDUFS6No5NDUFS3, NDUFA8, NDUFS1, NDUFA12, NDUFS5
NDUFAF1NDUFS7No9TIMMDC1, NDUFS1, NDUFA13, ACAD9, NDUFA8, NDUFA12, NDUFAF3, NDUFS5, NDUFS3
NDUFAF3NDUFV2No10NDUFS2, NDUFB10, NDUFA13, NDUFS8, NDUFS7, NDUFA8, SURF1, NDUFS5, NDUFS4, NDUFS3
NDUFAF3NDUFV1No11NDUFS2, NDUFB10, NDUFS5, ICT1, NDUFA13, NDUFS8, NDUFS7, NDUFA8, TIMMDC1, NDUFS4, NDUFS3
NDUFAF3NDUFA1No1NDUFA8
NDUFAF3FOXRED1No1NDUFS5
NDUFAF3NDUFA11No8NDUFS2, NDUFS8, NDUFS7, NDUFA8, NDUFB11, NDUFS5, NDUFS4, NDUFS3
NDUFAF3NDUFS1No13MYC, NDUFS2, NDUFB10, ICT1, NDUFA13, NDUFAF1, NDUFS7, NDUFA8, NDUFS5, ECSIT, NDUFS8, NDUFS4, NDUFS3
NDUFAF3NDUFS2Yes13NDUFS8, ECSIT, ICT1, MRPS21, NDUFS5, NDUFA13, NDUFS7, ACAD9, NDUFA8, TIMMDC1, NDUFS4, MYC, NDUFS3
NDUFAF3NDUFS3Yes18NDUFAF4, NDUFS8, ND6, NDUFB10, ICT1, NDUFB11, NDUFA13, NDUFS2, CYC1, MYC, ACAD9, NDUFAF1, SURF1, NDUFS7, NDUFS5, ECSIT, NDUFAF5, NDUFS4
NDUFAF3NDUFS4Yes9NDUFS2, NDUFB10, NDUFA13, NDUFS8, CYC1, NDUFA8, NDUFS7, NDUFS5, NDUFS3
NDUFAF3NDUFS6No7NDUFS2, NDUFS8, NDUFS7, NDUFA8, NDUFS5, NDUFS4, NDUFS3
NDUFAF3NDUFS7Yes13NDUFAF4, NDUFS2, NDUFB10, NDUFS5, NDUFA13, NDUFS8, NDUFS7, ACAD9, NDUFA8, TIMMDC1, NDUFAF5, NDUFS4, NDUFS3
NDUFV2NDUFV1Yes28ND1, NDUFS1, RMDN3, TPI1, NDUFS8, SDHA, NDUFA8, NDUFS5, VAPA, NOTCH2, NDUFA13, NDUFA2, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFS6, NDUFS2, RAB5C, NDUFA11, NDUFS4, NDUFA10, GOLT1B, NDUFB10, NDUFA9, ND5, SDHB, NDUFV3
NDUFV2NDUFA1No1NDUFA8
NDUFV2FOXRED1No1NDUFS5
NDUFV2NDUFA11Yes18NDUFS2, NDUFS5, NDUFS1, NDUFV1, NDUFS4, NDUFS8, NDUFA9, ND5, NDUFA10, NDUFB4, NDUFS7, NDUFA2, NDUFA12, NDUFS3, NDUFA8, NDUFA6, NDUFS6, NDUFV3
NDUFV2NDUFS1Yes26ND1, RMDN3, NDUFS8, NDUFA8, NDUFS5, VAPA, NDUFA13, NDUFS7, NDUFA12, NDUFV1, NDUFS2, RAB5C, NDUFA11, SLC25A3, NDUFS4, NDUFS6, NDUFS3, GOLT1B, NDUFB10, TCTN3, NDUFA9, COX2, MMGT1, SDHB, RAB7A, NDUFV3
NDUFV2NDUFS2Yes18GOLT1B, NDUFS4, NDUFS5, NDUFS1, TCTN3, NDUFA13, NDUFA9, NDUFA10, NDUFS8, NDUFS7, NDUFA11, NDUFA8, NDUFS3, NDUFA12, NDUFV1, NDUFS6, VAPA, SDHA
NDUFV2NDUFS3Yes23ND1, NDUFS1, NDUFS8, SDHA, NDUFS7, NDUFS5, NDUFA13, ND5, FN1, NDUFB4, NDUFA12, NDUFS6, NDUFA2, NDUFS2, NDUFA11, NDUFS4, NDUFV1, GOLT1B, NDUFB10, TCTN3, NDUFA9, SURF1, NDUFV3
NDUFV2NDUFS4Yes22NDUFS8, NDUFS1, ND1, NDUFA8, NDUFS5, VAPA, NDUFA13, NDUFA2, NDUFS7, NDUFB4, NDUFA12, NDUFS6, NDUFS2, NDUFA11, NDUFV1, NDUFS3, GOLT1B, NDUFB10, NDUFA9, ND5, SDHB, NDUFV3
NDUFV2NDUFS6Yes23NDUFS8, NDUFS1, RMDN3, SDHA, TJP1, NDUFS5, VAPA, NDUFS7, NDUFB4, NDUFA12, NDUFV1, NDUFS2, RAB5C, NDUFA11, NDUFS4, NDUFS3, GOLT1B, NDUFA9, NDUFA8, MMGT1, NDUFA2, RAB7A, NDUFV3
NDUFV2NDUFS7Yes15NDUFS2, NDUFB10, NDUFS5, NDUFS1, NDUFS4, NDUFA9, NDUFA13, NDUFS8, NDUFS7, NDUFA11, NDUFA8, NDUFA12, NDUFV1, NDUFS6, NDUFS3
NDUFV1NDUFA1No1NDUFA8
NDUFV1FOXRED1No1NDUFS5
NDUFV1NDUFA11Yes21NDUFS2, NDUFS1, NDUFV2, NDUFS5, NDUFS4, UQCRFS1, NDUFA9, ND5, NDUFS8, NDUFB4, NDUFS7, NDUFA2, NDUFA12, NDUFA10, NDUFB6, NDUFS3, NDUFA8, NDUFB8, NDUFS6, NDUFV3, UQCRB
NDUFV1NDUFS1Yes31BMPR1A, NDUFV2, RMDN3, TOMM40, ND1, ATP1B1, ATP6V0D1, NDUFS5, VAPA, CPT1A, NDUFA13, NDUFS7, NDUFS3, NDUFA12, NDUFS6, ATP5F1, NDUFS2, RAB5C, NDUFA11, NDUFA8, NDUFS4, ATP1A1, MTCH1, GOLT1B, NDUFB10, ICT1, NDUFA9, UQCRB, SDHB, NDUFS8, NDUFV3
NDUFV1NDUFS2Yes22NDUFS8, NDUFV2, SDHA, NDUFA8, NDUFS5, VAPA, NDUFS1, ICT1, NDUFA13, NDUFS7, NDUFA10, NDUFA12, NDUFS6, ADRB2, TIMMDC1, ATP5F1, NDUFA11, NDUFS4, HSPA1L, NDUFS3, GOLT1B, NDUFA9
NDUFV1NDUFS3Yes26NDUFS8, NPHP1, NDUFV2, ND1, ATP1B1, NDUFS5, NDUFB8, NDUFS1, ICT1, NDUFA13, NDUFA2, NDUFS7, NDUFB4, NDUFA12, NDUFS6, ADRB2, NDUFS2, NDUFA11, SDHA, NDUFB6, NDUFS4, GOLT1B, NDUFB10, NDUFA9, ND5, NDUFV3
NDUFV1NDUFS4Yes29ND1, NDUFV2, NDUFS8, UQCRB, NDUFS5, VAPA, VDAC2, NDUFS1, NDUFA13, NDUFA2, NDUFS7, NDUFB4, NDUFA12, NDUFS6, ATP5F1, NDUFS2, NDUFA11, NDUFA8, NDUFB8, ATP1A1, NDUFS3, GOLT1B, NDUFB10, ABCD3, ATP6V0D1, ND5, SDHB, NDUFA9, NDUFV3
NDUFV1NDUFS6Yes21GOLT1B, NDUFS1, NDUFV2, NDUFA12, RMDN3, NDUFA9, NDUFS8, NDUFB4, RAB5C, NDUFA11, NDUFA2, NDUFS7, ILF3, VAPA, NDUFA8, NDUFS3, NDUFS2, NDUFS4, NDUFS5, NDUFV3, SDHA
NDUFV1NDUFS7Yes17NDUFS2, NDUFB10, NDUFV2, ATP5F1, NDUFA12, NDUFA9, NDUFA13, NDUFS8, NDUFS7, NDUFA11, NDUFA8, NDUFS3, TIMMDC1, NDUFS5, NDUFS6, NDUFS4, NDUFS1
NDUFA1NDUFA11No1NDUFA8
NDUFA1NDUFS1No1NDUFA8
NDUFA1NDUFS2No1NDUFA8
NDUFA1NDUFS4No1NDUFA8
NDUFA1NDUFS6No1NDUFA8
NDUFA1NDUFS7No1NDUFA8
FOXRED1NDUFA11No1NDUFS5
FOXRED1NDUFS1No1NDUFS5
FOXRED1NDUFS2No4NXF1, SHMT2, NDUFS5, MOV10
FOXRED1NDUFS3No4NXF1, SHMT2, NDUFS5, MOV10
FOXRED1NDUFS4No1NDUFS5
FOXRED1NDUFS6No3NXF1, NDUFS5, MOV10
FOXRED1NDUFS7No1NDUFS5
NDUFA11NDUFS1Yes16NDUFS2, NDUFA12, NDUFV2, NDUFS4, NDUFA9, NDUFS8, NDUFS7, AFG3L2, NDUFA8, NDUFS6, NDUFS3, NDUFS5, NDUFB5, NDUFV1, NDUFV3, UQCRB
NDUFA11NDUFS2Yes13NDUFS8, NDUFV2, NDUFS1, NDUFA12, NDUFS4, NDUFA9, NDUFS7, NDUFA8, NDUFA10, NDUFS5, NDUFV1, NDUFS6, NDUFS3
NDUFA11NDUFS3Yes22NDUFS8, NDUFV2, NDUFB11, NDUFS5, NDUFB8, NDUFS1, NDUFB4, NDUFS7, NDUFA5, NDUFA12, NDUFV1, NDUFA2, ND4, NDUFB6, NDUFS4, NDUFS6, NDUFS2, NDUFA9, ND5, NDUFB3, NDUFB5, NDUFV3
NDUFA11NDUFS4Yes20NDUFB5, NDUFS2, NDUFS1, NDUFV2, NDUFB4, ND4, NDUFA9, NDUFS8, ND5, NDUFS7, NDUFB8, NDUFA2, NDUFA12, NDUFS3, NDUFA8, NDUFS5, NDUFV1, NDUFS6, NDUFV3, UQCRB
NDUFA11NDUFS6Yes16NDUFS2, NDUFS1, NDUFV2, NDUFB4, ND4, NDUFA9, NDUFS8, NDUFA8, NDUFS7, NDUFA2, NDUFA12, NDUFS3, NDUFS5, NDUFV1, NDUFS4, NDUFV3
NDUFA11NDUFS7Yes15NDUFS2, NDUFS1, NDUFV2, NDUFA12, NDUFS4, NDUFA9, NDUFS8, NDUFA5, NDUFS7, NDUFA8, NDUFS6, NDUFS5, NDUFB5, NDUFV1, NDUFS3
NDUFS1NDUFS2Yes24NDUFS8, NDUFV2, NDUFA8, MTCH2, NDUFS5, VAPA, ICT1, NDUFA13, NDUFS7, NDUFA12, NDUFS6, ECSIT, FBXO6, ATP5F1, NDUFA11, NDUFS4, NDUFV1, NDUFS3, GOLT1B, TCTN3, NDUFA9, NTRK1, MYC, CUL3
NDUFS1NDUFS3Yes34ND1, NDUFS5, NDUFV2, VCAM1, NDUFS8, TMEM126B, ATP1B3, MTCH2, EGFR, ICT1, HTT, NDUFA13, NDUFS7, NDUFA12, NDUFV1, ECSIT, NDUFS2, NDUFA11, UBC, NDUFAF1, ATP1B1, UQCRC2, NDUFS4, NDUFB5, GOLT1B, NDUFB10, TCTN3, NDUFA9, NDUFB9, NDUFS6, NDUFV3, NTRK1, MYC, CUL3
NDUFS1NDUFS4Yes26ND1, UQCRC2, NDUFV2, NDUFS8, ATP6V0D1, NDUFS5, VAPA, ATP5C1, NDUFA13, NDUFS7, NDUFA12, ATP1A1, ATP5F1, NDUFS2, NDUFA11, NDUFA8, NDUFS6, NDUFS3, GOLT1B, NDUFB10, NDUFV1, NDUFA9, UQCRB, SDHB, NDUFB5, NDUFV3
NDUFS1NDUFS6Yes19NDUFA11, GOLT1B, NDUFS4, NDUFS5, NDUFV2, RMDN3, NDUFA9, NDUFS8, NDUFS2, RAB5C, MMGT1, NDUFA8, NDUFS7, VAPA, NDUFA12, NDUFS3, NDUFV1, RAB7A, NDUFV3
NDUFS1NDUFS7Yes19NDUFB5, NDUFS2, NDUFB10, NDUFV2, ATP5F1, NDUFS5, NDUFS4, NDUFA9, NDUFA13, NDUFS8, NDUFS7, NDUFA11, NDUFA8, RHOT2, NDUFA12, NDUFV1, FBXO6, NDUFS6, NDUFS3
NDUFS2NDUFS3Yes30NDUFS8, NDUFS5, NDUFV2, LMAN2, SDHA, MTCH2, NDUFAF3, NXF1, SHMT2, NDUFS1, ICT1, NDUFA13, NDUFS7, NDUFA12, NDUFV1, SQSTM1, ADRB2, ECSIT, NDUFA11, NDUFS4, NDUFS6, MOV10, GOLT1B, TCTN3, NDUFA9, PARK2, ACAD9, NTRK1, MYC, CUL3
NDUFS2NDUFS4Yes21NDUFS8, GOLT1B, VAPA, ATP5F1, NDUFS1, NDUFV1, NDUFAF3, OGDH, PARK2, DLAT, NDUFS7, NDUFA11, NDUFA13, NDUFA8, APP, NDUFA12, NDUFS5, NDUFV2, NDUFA9, NDUFS6, NDUFS3
NDUFS2NDUFS6Yes17GOLT1B, NDUFV2, NDUFS1, NDUFS5, NDUFS4, NDUFA9, NDUFS8, NDUFS7, NDUFA11, NDUFA8, MOV10, NDUFA12, NDUFS3, NXF1, NDUFV1, VAPA, SDHA
NDUFS2NDUFS7Yes19NDUFA11, NDUFS8, NDUFV2, ATP5F1, NDUFA12, NDUFS4, NDUFAF3, NDUFA9, NDUFA13, NDUFS7, TIMMDC1, ACAD9, NDUFA8, NDUFS3, FBXO6, NDUFS5, NDUFV1, NDUFS6, NDUFS1
NDUFS3NDUFS4Yes27ND1, NDUFS5, NDUFV2, NDUFS8, CYC1, NDUFAF3, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFA12, NDUFV1, ND4, NDUFS2, NDUFA11, UQCRC2, NDUFB8, NDUFS6, GOLT1B, NDUFB10, NDUFA9, PARK2, NDUFA2, ND5, NDUFB5, NDUFV3
NDUFS3NDUFS6Yes20GOLT1B, NDUFS1, NDUFV2, NDUFS5, NDUFS4, NDUFA9, NDUFS8, NDUFB4, NDUFS7, NDUFA11, ND4, NDUFA7, NDUFA2, NDUFV3, NDUFA12, NDUFS2, NXF1, NDUFV1, MOV10, SDHA
NDUFS3NDUFS7Yes20NDUFA11, NDUFB5, NDUFS2, NDUFB10, NDUFS1, NDUFV2, NDUFAF4, NDUFS4, NDUFA12, NDUFA13, NDUFS8, NDUFS7, ACAD9, NDUFA5, NDUFA9, NDUFAF3, NDUFAF5, NDUFS5, NDUFV1, NDUFS6
NDUFS4NDUFS6Yes20GOLT1B, COX15, NDUFS1, NDUFV2, NDUFB4, ND4, NDUFA9, NDUFS8, NDUFA7, NDUFS7, NDUFA11, NDUFA2, NDUFA12, VAPA, NDUFA8, NDUFS3, NDUFS2, NDUFV1, NDUFS5, NDUFV3
NDUFS4NDUFS7Yes18NDUFS2, NDUFB10, NDUFV2, ATP5F1, NDUFA12, NDUFA9, NDUFA13, NDUFS8, NDUFS7, NDUFA11, NDUFA8, NDUFS6, NDUFS3, NDUFAF3, NDUFS5, NDUFB5, NDUFV1, NDUFS1
NDUFS6NDUFS7Yes14NDUFS2, NDUFV2, NDUFS1, NDUFA12, NDUFA9, NDUFS8, NDUFS7, NDUFA11, NDUFA8, MPV17, NDUFS5, NDUFV1, NDUFS4, NDUFS3

Direct interactions graph
Interactions graph (direct and indirect interactions, when direct are not available)

Interactions from BIOGRID - genetic
Interactions from STRING
Gene1Gene2Direct InteractionInteraction modeNumber of shared interactorsShared genes in interaction
NDUFB9NDUFB3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFAF4No-1UBC
NDUFB9NDUFAF1Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFV2Yesbinding44NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFC2-KCTD14, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFV1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9MT-ND3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9MT-ND5Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9MT-ND6Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFA8, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFA1Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFC2-KCTD14, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9FOXRED1No-1UBC
NDUFB9NDUFA11Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9MT-ND1Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFS1Yesbinding45NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFC2-KCTD14, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFS2Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFS3Yesbinding45NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFC2-KCTD14, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFS7Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFAF1Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFV2Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFV1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3MT-ND3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3MT-ND5Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3MT-ND6Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFA1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFA11Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3MT-ND1Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFS1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFS2Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFS3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3NDUFS7Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF4NDUFAF3Yesbinding0
NDUFAF4FOXRED1No-1UBC
NDUFAF4NDUFA11No-1UBC
NDUFAF4NDUFS1No-1UBC
NDUFAF4NDUFS3No-1UBC
NDUFAF4NDUFS7No-1UBC
NDUFAF1NDUFV2Yesbinding42NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFV1Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1MT-ND3Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1MT-ND5Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1MT-ND6No-41NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFA1Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFA11Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1MT-ND1Yesbinding42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFS1Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFS2Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFS3Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFS4Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFS6Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFAF1NDUFS7Yesbinding42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFV1Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2MT-ND3Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2MT-ND5Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2MT-ND6Yesbinding40NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFA1Yesbinding44NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFC2-KCTD14, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFA11Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2MT-ND1Yesbinding43NDUFS8, NDUFS1, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFS1Yesbinding44NDUFS8, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFC2-KCTD14, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFS2Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFS3Yesbinding44NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFC2-KCTD14, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFS4Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFS6Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV2NDUFS7Yesbinding43NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1MT-ND3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1MT-ND5Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1MT-ND6Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFS6, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1NDUFA1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1NDUFA11Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1MT-ND1Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1NDUFS1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1NDUFS2Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1NDUFS3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFV1NDUFS7Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3MT-ND5Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3MT-ND6Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3NDUFA1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3NDUFA11Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3MT-ND1Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3NDUFS1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3NDUFS2Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3NDUFS3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND3NDUFS7Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5MT-ND6Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5NDUFA1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5NDUFA11Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5MT-ND1Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5NDUFS1Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5NDUFS2Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5NDUFS3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND5NDUFS7Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6NDUFA1Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6NDUFA11Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6MT-ND1Yesbinding40NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6NDUFS1Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6NDUFS2Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6NDUFS3Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6NDUFS4Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6NDUFS6Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND6NDUFS7Yesbinding40NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA5, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFS6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA1NDUFA11Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA1MT-ND1Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA1NDUFS1Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFC2-KCTD14, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA1NDUFS2Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA1NDUFS3Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFC2-KCTD14, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA1NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA1NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA1NDUFS7Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
FOXRED1NDUFA11No-1UBC
FOXRED1NDUFS1No-1UBC
FOXRED1NDUFS3No-1UBC
FOXRED1NDUFS7No-1UBC
NDUFA11MT-ND1Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA11NDUFS1Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA11NDUFS2Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA11NDUFS3Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA11NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA11NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFA11NDUFS7Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND1NDUFS1Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND1NDUFS2Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND1NDUFS3Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND1NDUFS4Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND1NDUFS6Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
MT-ND1NDUFS7Yesbinding43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS1NDUFS2Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS1NDUFS3Yesbinding45NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFC2-KCTD14, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS1NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS1NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS1NDUFS7Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS2NDUFS3Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS2NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS2NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS2NDUFS7Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS3NDUFS4Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS3NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS3NDUFS7Yesbinding44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, UBC, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS4NDUFS6Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS4NDUFS7Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, MT-ND4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFS6NDUFS7Yesbinding43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFV1, NDUFA10, NDUFS2, NDUFB10, NDUFB2, MT-ND5, NDUFS4, MT-ND4, NDUFB9, NDUFA2, NDUFAF1, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2

Direct interactions graph
Interactions graph (direct and indirect interactions, when direct are not available)

Interactions from CORUM
Gene1Gene2Direct InteractionComplexesNumber of shared interactorsShared genes in interaction
NDUFB9NDUFB3YesRespiratory chain complex I (beta subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA6, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, MT-ND4, NDUFA8, NDUFA2, NDUFS6, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9NDUFAF1No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFB9NDUFV2YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFA3, NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFV1, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFV1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFA6, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9MT-ND3YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFA3, NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFV1, NDUFB7, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9MT-ND5YesRespiratory chain complex I (beta subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB9MT-ND6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFV1, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFA3, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFA1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFA6, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFA11YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFA6, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9MT-ND1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFA6, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFS1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFA3, NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFV1, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFS2YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFA12, NDUFA6, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFS3YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFA12, NDUFA6, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFS4YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA7, NDUFS1, NDUFA13, MT-ND5, NDUFS7, NDUFB4, NDUFS3, NDUFA12, NDUFA6, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFS6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB9NDUFS7YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, MT-ND5, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFA12, NDUFA6, NDUFB7, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFA8, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFAF1No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFB3NDUFV2YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFV1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3MT-ND3YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3MT-ND5YesRespiratory chain complex I (beta subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA9, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, MT-ND4, MT-ND2, NDUFA2, NDUFS6, NDUFB5, NDUFA4, NDUFV3, NDUFC2
NDUFB3MT-ND6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFA1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFA11YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3MT-ND1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFS1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFS2YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFS3YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFS4YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFS6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFB3NDUFS7YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFAF1NDUFV2No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1NDUFV1No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1MT-ND3YesRespiratory chain complex I (incomplete intermediate ND1, ND2, ND3, CIA30 assembly), mitochondrial8NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1MT-ND5No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1MT-ND6No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1NDUFA1YesEcsit complex (ECSIT, MT-CO2, NDUFA1, MT-ND1, TRAF6, NDUFAF1)11ECSIT, MT-ND3, NDUFA9, MT-ND2, TRAF6, MT-CO2, NDUFS7, MT-ND1, NDUFB6, NDUFA6, NDUFS3
NDUFAF1NDUFA11No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1MT-ND1YesEcsit complex (ECSIT, MT-CO2, NDUFA1, MT-ND1, TRAF6, NDUFAF1);Respiratory chain complex I (incomplete intermediate ND1, ND2, ND3, CIA30 assembly), mitochondrial;Respiratory chain complex I (early intermediate NDUFAF1 assembly), mitochondrial;Respiratory chain complex I (incomplete NDUFAF1 assembly), mitochondrial11ECSIT, MT-ND3, NDUFA9, MT-ND2, TRAF6, MT-CO2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1NDUFS1No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1NDUFS2No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1NDUFS3YesRespiratory chain complex I (early intermediate NDUFAF1 assembly), mitochondrial;Ecsit complex (ECSIT, NDUFS3, NDUFAF1)9ECSIT, MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1
NDUFAF1NDUFS4No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1NDUFS6No-9MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFS7, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFAF1NDUFS7YesRespiratory chain complex I (early intermediate NDUFAF1 assembly), mitochondrial8MT-ND3, NDUFA9, MT-ND1, MT-ND2, NDUFB6, NDUFA6, NDUFA1, NDUFS3
NDUFV2NDUFV1YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2MT-ND3YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2MT-ND5YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2MT-ND6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2NDUFA1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, NDUFB9, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2NDUFA11YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2MT-ND1YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, NDUFB11, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2NDUFS1YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2NDUFS2YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2NDUFS3YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2NDUFS4YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (intermediate II/230kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2NDUFS6YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV2NDUFS7YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (intermediate II/230kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFS1, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1MT-ND3YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1MT-ND5YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1MT-ND6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1NDUFA1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1NDUFA11YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1MT-ND1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1NDUFS1YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1NDUFS2YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1NDUFS3YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1NDUFS4YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1NDUFS6YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFV1NDUFS7YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3MT-ND5YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3MT-ND6YesRespiratory chain complex I (gamma subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3NDUFA1YesRespiratory chain complex I (gamma subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, NDUFB11, NDUFB9, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, MT-ND2, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, MT-ND1, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFA4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3NDUFA11YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3MT-ND1YesRespiratory chain complex I (gamma subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate ND1, ND2, ND3, CIA30 assembly), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, NDUFB11, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, MT-ND2, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3NDUFS1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3NDUFS2YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3NDUFS3YesRespiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, MT-ND2, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFV1, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, NDUFAF1, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3NDUFS4YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3NDUFS6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND3NDUFS7YesRespiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5MT-ND6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5NDUFA1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, NDUFB9, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, MT-ND1, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5NDUFA11YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5MT-ND1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5NDUFS1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5NDUFS2YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5NDUFS3YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5NDUFS4YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5NDUFS6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND5NDUFS7YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, NDUFC1, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6NDUFA1YesRespiratory chain complex I (gamma subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, NDUFB9, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND1, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6NDUFA11YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6MT-ND1YesRespiratory chain complex I (gamma subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6NDUFS1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6NDUFS2YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6NDUFS3YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6NDUFS4YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6NDUFS6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND6NDUFS7YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA1NDUFA11YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA1MT-ND1YesEcsit complex (ECSIT, MT-CO2, NDUFA1, MT-ND1, TRAF6, NDUFAF1);Respiratory chain complex I (gamma subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial46NDUFS8, NDUFV2, NDUFB11, NDUFB9, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFA3, NDUFS1, MT-ND2, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, ECSIT, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, TRAF6, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFA4, MT-CO2, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA1NDUFS1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA1NDUFS2YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA1NDUFS3YesRespiratory chain complex I (holoenzyme), mitochondrial44NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFB7, NDUFA8, NDUFA6, ECSIT, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA1NDUFS4YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA1NDUFS6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, MT-ND1, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA1NDUFS7YesRespiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFS4, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA11MT-ND1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA11NDUFS1YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA11NDUFS2YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA11NDUFS3YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA11NDUFS4YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA11NDUFS6YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, MT-ND1, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFA11NDUFS7YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND1NDUFS1YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND1NDUFS2YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (intermediate V/380kD and VI/480kD), mitochondrial;Respiratory chain complex I (intermediate IV/310kD), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND1NDUFS3YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (intermediate V/380kD and VI/480kD), mitochondrial;Respiratory chain complex I (early intermediate NDUFAF1 assembly), mitochondrial;Respiratory chain complex I (intermediate IV/310kD), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial44NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFB7, NDUFA8, NDUFA6, ECSIT, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND1NDUFS4YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND1NDUFS6YesRespiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
MT-ND1NDUFS7YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (early intermediate NDUFAF1 assembly), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, NDUFB11, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS1NDUFS2YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS1NDUFS3YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS1NDUFS4YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS1NDUFS6YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS1NDUFS7YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, NDUFB9, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFA3, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFV1, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA6, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFS4, NDUFA4, MT-ND2, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS2NDUFS3YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (intermediate V/380kD and VI/480kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (intermediate I/200kD and III/250kD), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial;Respiratory chain complex I (intermediate IV/310kD), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS2NDUFS4YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS2NDUFS6YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS2NDUFS7YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS3NDUFS4YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFS7, NDUFB4, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS3NDUFS6YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS3NDUFS7YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (early intermediate NDUFAF1 assembly), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial43NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFAF1, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS4NDUFS6YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFS7, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS4NDUFS7YesRespiratory chain complex I (intermediate VII/650kD), mitochondrial;Respiratory chain complex I (intermediate II/230kD), mitochondrial;Respiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFA7, NDUFB4, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFA4, NDUFB9, NDUFA2, NDUFS6, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2
NDUFS6NDUFS7YesRespiratory chain complex I (lambda subunit) mitochondrial;Respiratory chain complex I (incomplete intermediate), mitochondrial;Respiratory chain complex I (holoenzyme), mitochondrial42NDUFS8, NDUFV2, MT-ND1, MT-ND2, NDUFS5, NDUFA1, MT-ND4L, NDUFB1, NDUFS1, NDUFA13, NDUFB4, NDUFA7, NDUFS3, NDUFB7, NDUFA8, NDUFA6, NDUFA12, MT-ND3, NDUFA5, NDUFAB1, NDUFA11, NDUFC1, MT-ND6, NDUFB11, NDUFB6, NDUFB8, NDUFA3, NDUFA10, NDUFS2, NDUFB10, MT-ND5, NDUFB2, NDUFV1, NDUFS4, NDUFA4, NDUFB9, NDUFA2, NDUFB3, NDUFB5, NDUFA9, NDUFV3, NDUFC2

Direct interactions graph
Interactions graph (direct and indirect interactions, when direct are not available)

Interactions from CENSUS
Gene1Gene2Direct InteractionNumber of shared interactorsShared genes in interaction
NDUFB9NDUFAF3No1ABCC1
NDUFB9NDUFV2No2SDHB, NDUFS1
NDUFB9NDUFV1No4ILF3, NDUFB10, HSPA1L, NDUFS1
NDUFB9MT-ND5No5ABCC1, NDUFA5, ABCC2, MPV17, NDUFS1
NDUFB9MT-ND1No4NDUFA5, ILF3, MPV17, NDUFS1
NDUFB9NDUFS1Yes6ATP5B, NDUFB10, NDUFA12, ATP5C1, SDHB, NDUFB5
NDUFB9NDUFS2No2HSPA1L, NDUFS1
NDUFB9NDUFS3No1NDUFA5
NDUFB9NDUFS4No3NDUFB5, NDUFA12, ATP5O
NDUFB9NDUFS6No3NDUFA2, ILF3, MPV17
NDUFB9NDUFS7No5NDUFB10, NDUFB5, ATP5F1, MPV17, NDUFS1
NDUFAF3NDUFV2No2SURF1, NDUFS8
NDUFAF3NDUFV1No1NDUFS8
NDUFAF3MT-ND5No2ABCC1, NDUFS8
NDUFAF3MT-ND1No1NDUFS8
NDUFAF3NDUFS1No1NDUFS8
NDUFAF3NDUFS2No2NDUFS8, MRPS21
NDUFAF3NDUFS3No2SURF1, NDUFS8
NDUFAF3NDUFS4Yes1CYC1
NDUFAF3NDUFS6No2NDUFS8, NDUFS4
NDUFAF3NDUFS7No2NDUFS8, NDUFS4
NDUFV2NDUFV1Yes9NOTCH2, MT-ND5, NDUFS1, NDUFS2, MT-ND1, NDUFS7, SDHA, NDUFS8, NDUFS3
NDUFV2MT-ND5Yes8NDUFS2, NDUFS1, NDUFS8, SLC25A3, NDUFS7, MT-ND1, NDUFV1, NDUFS3
NDUFV2MT-ND1Yes8NDUFS2, MT-ND5, NDUFS1, NDUFS8, SLC25A3, NDUFS7, NDUFV1, NDUFS3
NDUFV2NDUFS1Yes8NDUFS2, MT-ND5, NDUFS8, MT-ND1, NDUFS7, SDHB, NDUFV1, NDUFV3
NDUFV2NDUFS2Yes8NDUFS8, MT-ND5, NDUFS1, NDUFS7, MT-ND1, NDUFV1, NDUFS3, SDHA
NDUFV2NDUFS3Yes8NDUFS2, MT-ND5, NDUFS8, MT-ND1, SURF1, NDUFS7, SDHA, NDUFV1
NDUFV2NDUFS4No1NDUFS7
NDUFV2NDUFS6No6NDUFS2, NDUFB4, NDUFS8, NDUFS7, TJP1, SDHA
NDUFV2NDUFS7Yes7NDUFS2, MT-ND5, NDUFS1, NDUFS8, MT-ND1, NDUFV1, NDUFS3
NDUFV1MT-ND5Yes7NDUFS2, NDUFV2, NDUFS1, NDUFS8, NDUFS7, MT-ND1, NDUFS3
NDUFV1MT-ND1Yes8NDUFS2, MT-ND5, NDUFS1, NDUFS8, NDUFS7, ILF3, NDUFV2, NDUFS3
NDUFV1NDUFS1Yes9NDUFS2, NDUFB10, NDUFV2, MT-ND5, NDUFA9, NDUFS8, MT-ND1, NDUFS7, CPT1A
NDUFV1NDUFS2Yes9NDUFS8, MT-ND5, NDUFS1, NDUFS7, MT-ND1, NDUFV2, HSPA1L, NDUFS3, SDHA
NDUFV1NDUFS3Yes7NDUFS2, MT-ND5, NDUFV2, NDUFS8, NDUFS7, MT-ND1, SDHA
NDUFV1NDUFS4No2ABCD3, NDUFS7
NDUFV1NDUFS6No5NDUFS8, NDUFS7, ILF3, NDUFS2, SDHA
NDUFV1NDUFS7Yes8NDUFS2, NDUFB10, NDUFV2, MT-ND5, NDUFS8, MT-ND1, NDUFS3, NDUFS1
MT-ND5MT-ND1Yes10NDUFS2, NDUFS1, NDUFV2, NDUFS8, SLC25A3, NDUFA5, NDUFS7, MPV17, NDUFV1, NDUFS3
MT-ND5NDUFS1Yes6NDUFS2, NDUFV2, NDUFS8, NDUFS7, MT-ND1, NDUFV1
MT-ND5NDUFS2Yes7NDUFS8, NDUFV2, NDUFS1, NDUFS7, MT-ND1, NDUFV1, NDUFS3
MT-ND5NDUFS3Yes7NDUFS2, NDUFV2, NDUFS8, NDUFS7, NDUFA5, MT-ND1, NDUFV1
MT-ND5NDUFS4No3DLAT, UQCRB, NDUFS7
MT-ND5NDUFS6No4NDUFS8, NDUFS7, NDUFS2, MPV17
MT-ND5NDUFS7Yes8NDUFS2, NDUFS1, NDUFV2, NDUFS8, MT-ND1, MPV17, NDUFV1, NDUFS3
MT-ND1NDUFS1Yes7NDUFS2, NDUFV2, MT-ND5, NDUFS8, NDUFS7, RHOT2, NDUFV1
MT-ND1NDUFS2Yes7NDUFS8, MT-ND5, NDUFS1, NDUFS7, NDUFV1, NDUFV2, NDUFS3
MT-ND1NDUFS3Yes7NDUFS2, NDUFV2, MT-ND5, NDUFS8, NDUFS7, NDUFA5, NDUFV1
MT-ND1NDUFS4No1NDUFS7
MT-ND1NDUFS6No5NDUFS8, NDUFS7, ILF3, NDUFS2, MPV17
MT-ND1NDUFS7Yes9NDUFS2, NDUFV2, MT-ND5, NDUFS8, RHOT2, NDUFS3, MPV17, NDUFV1, NDUFS1
NDUFS1NDUFS2Yes6NDUFS8, MT-ND5, NDUFV2, NDUFS7, MT-ND1, NDUFV1
NDUFS1NDUFS3No7NDUFS2, MT-ND5, NDUFV2, NDUFS8, NDUFS7, MT-ND1, NDUFV1
NDUFS1NDUFS4No3NDUFB5, NDUFS7, NDUFA12
NDUFS1NDUFS6No3NDUFS8, NDUFS2, NDUFS7
NDUFS1NDUFS7Yes9NDUFS2, NDUFB10, NDUFV2, MT-ND5, NDUFS8, MT-ND1, RHOT2, NDUFB5, NDUFV1
NDUFS2NDUFS3Yes7NDUFS8, MT-ND5, NDUFV2, NDUFS7, MT-ND1, NDUFV1, SDHA
NDUFS2NDUFS4No2NDUFS6, NDUFS7
NDUFS2NDUFS6Yes3NDUFS8, NDUFS7, SDHA
NDUFS2NDUFS7Yes8NDUFS8, MT-ND5, NDUFS1, MT-ND1, NDUFV1, NDUFV2, NDUFS6, NDUFS3
NDUFS3NDUFS4No1NDUFS7
NDUFS3NDUFS6No4NDUFS8, NDUFS7, NDUFS2, SDHA
NDUFS3NDUFS7Yes6NDUFS2, MT-ND5, NDUFV2, NDUFS8, MT-ND1, NDUFV1
NDUFS4NDUFS6Yes2COX15, NDUFS7
NDUFS4NDUFS7Yes2NDUFB5, NDUFS6
NDUFS6NDUFS7Yes4NDUFS2, NDUFS8, NDUFS4, MPV17

Direct interactions graph
Interactions graph (direct and indirect interactions, when direct are not available)

Interactions from PDB
Interactions from manually curated literature
KEGG pathways annotation: shared terms / NET-GE enrichment

Shared terms

KEGG termKEGG term IDICNumber of genes with the same termGenes
Metabolic pathwayshsa011002.4916NDUFS2, MT-ND3, MT-ND5, NDUFS4, MT-ND6, MT-ND1, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Parkinson's diseasehsa050125.5916NDUFS2, MT-ND3, MT-ND5, NDUFS4, MT-ND6, MT-ND1, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Oxidative phosphorylationhsa001905.6916NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFB9, MT-ND1, NDUFS7, NDUFA11, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Huntington's diseasehsa050165.1712NDUFS2, NDUFV2, NDUFS1, NDUFS4, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFB3, NDUFV1, NDUFA1, NDUFS3
Alzheimer's diseasehsa050105.3412NDUFS2, NDUFV2, NDUFS1, NDUFS4, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFB3, NDUFV1, NDUFA1, NDUFS3
Non-alcoholic fatty liver disease (NAFLD)hsa049325.5112NDUFS2, NDUFV2, NDUFS1, NDUFS4, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFB3, NDUFV1, NDUFA1, NDUFS3

NET-GE enrichment

Term New enriched termICP valueGenes
Human DiseasesNEW1.540.013NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFB9, MT-ND1, NDUFS7, NDUFA11, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Neurodegenerative diseasesNEW4.270.0NDUFS2, MT-ND3, MT-ND5, NDUFS4, MT-ND6, MT-ND1, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Global and overview mapsNEW2.470.0NDUFS2, NDUFV2, MT-ND3, NUBPL, NDUFS4, MT-ND5, NDUFB9, MT-ND1, NDUFS7, NDUFA11, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFA1, NDUFS1
Endocrine and metabolic diseasesNEW4.750.0NDUFS2, NDUFV2, MT-ND3, NDUFS4, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFA1, NDUFS1
MetabolismNEW2.060.0NDUFS2, NDUFV2, MT-ND3, NUBPL, NDUFS4, MT-ND5, NDUFB9, MT-ND1, NDUFS7, NDUFA11, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFA1, NDUFS1
Oxidative phosphorylation (hsa00190) -5.690.0NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFB9, MT-ND1, NDUFS7, NDUFA11, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Metabolic pathways (hsa01100) -2.490.0NDUFS2, MT-ND3, MT-ND5, NUBPL, NDUFS4, MT-ND6, MT-ND1, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Energy metabolismNEW5.420.0NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFB9, MT-ND1, NDUFS7, NDUFA11, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Non-alcoholic fatty liver disease (NAFLD) (hsa04932) -5.510.0NDUFS2, NDUFV2, NDUFS1, NDUFS4, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFB3, NDUFV1, NDUFA1, NDUFS3
Huntington's disease (hsa05016) -5.170.0NDUFS2, NDUFV2, NDUFS1, NDUFS4, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFB3, NDUFV1, NDUFA1, NDUFS3
Alzheimer's disease (hsa05010) -5.340.0NDUFS2, NDUFS1, NDUFV2, NDUFS4, MT-ND1, NDUFA11, NDUFB9, NDUFS6, NDUFS7, NDUFB3, NDUFV1, NDUFA1, NDUFS3
Parkinson's disease (hsa05012) -5.590.0NDUFS2, MT-ND3, MT-ND5, NDUFS4, MT-ND6, MT-ND1, NDUFS7, NDUFA11, NDUFB9, NDUFS6, NDUFS3, NDUFB3, NDUFV1, NDUFV2, NDUFA1, NDUFS1
REACTOME pathways annotation: shared terms / NET-GE enrichment

Shared terms

REACTOME termREACTOME term IDICNumber of genes with the same termGenes
MetabolismR-HSA-14307282.3421NDUFA11, NDUFS2, NDUFV2, MT-ND3, NDUFS4, NDUFAF3, MT-ND5, NDUFA1, MT-ND6, NDUFS7, NDUFAF4, NDUFAF2, NDUFB9, NDUFS3, NDUFB3, NDUFAF5, NDUFAF6, NDUFV1, MT-ND1, NDUFS6, NDUFS1
The citric acid (TCA) cycle and respiratory electron transportR-HSA-14285175.7121NDUFA11, NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFAF3, NDUFB9, MT-ND1, NDUFS7, NDUFAF4, NDUFAF6, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFAF5, NDUFAF2, NDUFV1, NDUFV2, NDUFA1, NDUFS1
Respiratory electron transportR-HSA-6111056.4421NDUFA11, NDUFS2, NDUFV2, MT-ND3, NDUFS4, NDUFAF3, NDUFA1, MT-ND5, NDUFB9, NDUFAF4, NDUFAF2, MT-ND6, NDUFS7, NDUFS3, NDUFB3, NDUFAF5, NDUFAF6, NDUFV1, MT-ND1, NDUFS6, NDUFS1
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins.R-HSA-1632006.1221NDUFA11, NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFS3, NDUFA1, MT-ND6, MT-ND1, NDUFAF4, NDUFAF2, NDUFB9, NDUFAF3, NDUFS7, NDUFB3, NDUFAF5, NDUFAF6, NDUFV1, NDUFV2, NDUFS6, NDUFS1

NET-GE enrichment

Term New enriched termICP valueGenes
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (R-HSA-163200) -6.120.0NDUFA11, NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFS3, NDUFA1, MT-ND6, MT-ND1, NDUFAF4, NDUFAF2, NDUFB9, NDUFAF3, NDUFS7, NDUFB3, NDUFAF5, NDUFAF6, NDUFV1, NDUFV2, NDUFS6, NDUFS1
Respiratory electron transport (R-HSA-611105) -6.440.0NDUFA11, NDUFS2, NDUFV2, MT-ND3, NDUFS4, NDUFAF3, NDUFA1, MT-ND5, NDUFB9, NDUFAF4, NDUFAF2, MT-ND6, NDUFS7, NDUFS3, NDUFB3, NDUFAF5, NDUFAF6, NDUFV1, MT-ND1, NDUFS6, NDUFS1
Metabolism (R-HSA-1430728) -2.340.0NDUFV2, MT-ND1, NDUFB9, NDUFAF3, NDUFAF6, NDUFA1, NDUFS1, NDUFS7, NDUFAF4, NUBPL, NDUFAF2, NDUFS6, MT-ND3, NDUFA11, MT-ND6, NDUFS4, NDUFAF5, NDUFS3, NDUFS2, MT-ND5, NDUFV1, NDUFB3
The citric acid (TCA) cycle and respiratory electron transport (R-HSA-1428517) -5.710.0NDUFA11, NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFAF3, NDUFB9, MT-ND1, NDUFS7, NDUFAF4, NDUFAF6, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFAF5, NDUFAF2, NDUFV1, NDUFV2, NDUFA1, NDUFS1
GO - molecular function annotation: shared terms / NET-GE enrichment

Shared terms

GOICNumber of genes with the same GOGenes
catalytic activity (GO:0003824) 1.0519NDUFS2, MT-ND3, MT-ND5, NDUFS4, NDUFS1, MT-ND6, FOXRED1, MT-ND1, NDUFAF6, NDUFB9, NDUFS6, NDUFS7, NDUFB3, NDUFAF5, NDUFAF2, NDUFV1, NDUFV2, NDUFA1, NDUFS3
oxidoreductase activity (GO:0016491) 3.1217FOXRED1, NDUFV2, MT-ND3, NDUFS4, MT-ND5, NDUFB9, NDUFS7, MT-ND6, NDUFS6, NDUFS3, NDUFB3, NDUFAF2, NDUFS2, NDUFV1, MT-ND1, NDUFA1, NDUFS1
NADH dehydrogenase (ubiquinone) activity (GO:0008137) 5.9316NDUFS2, NDUFV2, MT-ND3, NDUFS4, MT-ND5, NDUFB9, MT-ND1, NDUFAF2, MT-ND6, NDUFS6, NDUFS7, NDUFB3, NDUFS3, NDUFV1, NDUFA1, NDUFS1
oxidoreductase activity, acting on NAD(P)H (GO:0016651) 5.1316NDUFS2, MT-ND3, MT-ND5, NDUFS4, MT-ND6, MT-ND1, NDUFS7, NDUFB9, NDUFS6, NDUFS3, NDUFB3, NDUFAF2, NDUFV1, NDUFV2, NDUFA1, NDUFS1